Skeletal AM Questions

 

 

1:  Regarding desmoplastic fibroma, please answer the following with TRUE or FALSE.

a.

T or F

Desmoplastic fibroma is a malignant neoplasm.
b.

T or F

The most common site of occurence is the ilium.
c.

T or F

Curretage is the treatment of choice.
d.

T or F

"Pseudo-trabeculae" are a classic feature of desmoplastic fibroma..

 

 

 

 

 

 

 

 

 

2:  Please answer EACH of the following with TRUE or FALSE.

a.

T or F

Ewings sarcoma is typically a tumor of middle-age and beyond.
b.

T or F

Tubular bones are most commonly affected in Ewings sarcoma in patients under 20 years old, with flat bones most commonly affected in those older than 20.
c.

T or F

In Ewings sarcoma, bone metastases are uncommon and unlike the primary tumor, are usually blastic when they do occur.
d.

T or F

The vast majority of occurrences of Ewings sarcoma in the long bones are of the central diaphyseal type..

 

 

 

 

 

 

 

 

 

 

3:  Please answer the following with TRUE or FALSE.

a.

T or F

Achondroplasia is the most common type of short limb skeletal dysplasia which shortens stature.
b.

T or F

Achondroplasia is an autosomal recessive defect.
c.

T or F

The short pedicles of achondroplasia lead to spinal stenosis and paraplegia more than 15% of patients.
d.

T or F

Hydrocephalus is an uncommon complication in patients with achondroplasia.
e.

T or F

About 90% of the cases of achondroplasia occur from a spontaneous mutation in patients with normal parents.

 

 

 

 

 

 

 

 

 

4:  Which is the most severe form of short-limbed dwarfism? Please pick the BEST answer.

A

Hypochondroplasia

B

Achondroplasia

C

Thanatophoric dwarfism

D

Homozygous achondroplasia

 

 

 

 

 

 

 

 

 

 

 

5:  Please answer EACH of the following with TRUE or FALSE

a.

T or F

An osteochondroma is a bony projection with a cartilaginous cap arising from a bone preformed in cartilage.
b.

T or F

Malignant degeneration of osteochondroma to chondrosarcoma occurs in up to 20% of patients with hereditary multiple exostoses.
c.

T or F

The cortex and medullary cavity of the host bone are not continuous with the osteochondroma.
d.

T or F

The most common sites for osteochondroma are the hands and feet.
e.

T or F

Almost all pseudoanerysms complicating osteochondromas arise from the popliteal artery.
f.

T or F

Benign osteochondromas generally do not demonstrate continued growth after skeletal maturity.